64| Spina Bifida and Hydrocephalus – With Dr. Christine Koterba

Approximately one in every 2,800 babies are born with spina bifida each year.  Spina bifida is related to multiple physical and neurological symptoms including hydrocephalus, which differs from its presentation in older adults.  Today, John and Ryan talk with Christine Koterba, Ph.D., ABPP-CN, about spina bifida, hydrocephalus, and how neuropsychologists can contribute to the care of children with these disorders.

Topics Covered

  • Basic definition of hydrocephalus
  • Hydrocephalus as a disconnection syndrome
  • Basic definition of normal pressure hydrocephalus (NPH) and its prevalence across the lifespan
  • Treatment for NPH
  • Differentiating between atrophy in NPH and other neurodegenerative disorders
  • Different types of NPH
  • Distinctions between primary and secondary types of hydrocephalus
  • Disorders related to hydrocephalus in pediatric populations
  • Relationship of prematurity to intraventricular hemorrhage and hydrocephalus
  • Basic definition of spina bifida as well as a review of different types
  • Chiari malformation and its relationship with spina bifida
  • Spina bifida and its relationship to paralysis and/or paresis
  • The shunting process
  • Neuroimaging tools used to diagnose hydrocephalus
  • Characteristics of a prototypical referral for a child with hydrocephalus due to a medical condition such as spina bifida
  • Typical neuropsychological examination of a child with hydrocephalus due to a medical condition such as spina bifida
  • Social and emotional symptoms in hydrocephalus due to a medical condition such as spina bifida
  • Resources to provide parents and patients

About Chrissie

Christine (“Chrissie”) Koterba, Ph.D., ABPP-CN, is a clinical neuropsychologist specializing in pediatrics at Nationwide Children’s Hospital.  She is also a Clinical Assistant Professor of Pediatrics at the Ohio State University.

Selected Resources

Spina Bifida Association

Hydrocephalus Association

Got Transition

Centers for Disease Control and Prevention: Spina Bifida

Selected References

Akbari, S. H. A., Holekamp, T. F., Murphy, T. M., Mercer, D., Leonard, J. R., Smyth, M. D., … & Limbrick, D. D. (2015). Surgical management of complex multiloculated hydrocephalus in infants and children. Child’s Nervous System, 31(2), 243-249.

Alabi, N. B., Thibadeau, J., Wiener, J. S., Conklin, M. J., Dias, M. S., Sawin, K. J., & Valdez, R. (2018). Surgeries and health outcomes among patients with spina bifida. Pediatrics, 142(3). https://doi.org/10.1542/peds.2017-3730

Beuriat, P. A., Puget, S., Cinalli, G., Blauwblomme, T., Beccaria, K., Zerah, M., & Sainte-Rose, C. (2017). Hydrocephalus treatment in children: long-term outcome in 975 consecutive patients. Journal of Neurosurgery: Pediatrics, 20(1), 10-18.

Copp, A. J., Adzick, N. S., Chitty, L. S., Fletcher, J. M., Holmbeck, G. N., & Shaw, G. M. (2015). Spina bifida. Nature reviews Disease primers, 1(1), 1-18.

Fletcher, J. M., Brookshire, B. L., Landry, S. H., Bohan, T. P., Davidson, K. C., Francis, D. J., … & Morris, R. D. (1996). Attentional skills and executive functions in children with early hydrocephalus. Developmental Neuropsychology, 12(1), 53-76.

Foltz, E. L., & Shurtleff, D. B. (1963). Five-year comparative study of hydrocephalus in children with and without operation (113 cases). Journal of Neurosurgery, 20(12), 1064-1079.

Kahle, K. T., Kulkarni, A. V., Limbrick Jr, D. D., & Warf, B. C. (2016). Hydrocephalus in children. The lancet, 387(10020), 788-799.

Phillips, L. A., Burton, J. M., & Evans, S. H. (2017). Spina bifida management. Current Problems in Pediatric and Adolescent Health Care, 47(7), 173-177.

Rekate, H. L., & Blitz, A. M. (2016). Hydrocephalus in children. In Handbook of clinical neurology (Vol. 136, pp. 1261-1273). Elsevier.

Simon, T. D., Riva-Cambrin, J., Srivastava, R., Bratton, S. L., Dean, J. M., & Kestle, J. R. (2008). Hospital care for children with hydrocephalus in the United States: utilization, charges, comorbidities, and deaths. Journal of Neurosurgery: Pediatrics, 1(2), 131-137.

Wills, K. W. (1993). Neuropsychological functioning in children with spina bifida and/or hydrocephalus. Journal of Clinical Child Psychology, 22(2), 247-265.

Episodes

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